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DeCS
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Descriptor English:
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Arrhythmogenic Right Ventricular Dysplasia
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Descriptor Spanish:
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Displasia Ventricular Derecha Arritmogénica
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Descriptor Portuguese:
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Displasia Arritmogênica Ventricular Direita
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Synonyms English:
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ARVD-C
Arrhythmogenic Right Ventricular Cardiomyopathy
Arrhythmogenic Right Ventricular Cardiomyopathy Dysplasia
Arrhythmogenic Right Ventricular Cardiomyopathy-Dysplasia
Arrhythmogenic Right Ventricular Dysplasia-Cardiomyopathy
Right Ventricular Dysplasia, Arrhythmogenic
Ventricular Dysplasia, Right, Arrhythmogenic
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Tree Number:
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C14.240.400.145
C14.280.238.028
C14.280.400.145
C16.131.240.400.145
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Definition English:
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A congenital cardiomyopathy that is characterized by infiltration of adipose and fibrous tissue into the RIGHT VENTRICLE wall and loss of myocardial cells. Primary injuries usually are at the free wall of right ventricular and right atria resulting in ventricular and supraventricular arrhythmias. |
History Note English:
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98
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Allowable Qualifiers English:
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Record Number:
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33360
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Unique Identifier:
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D019571
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Occurrence in VHL:
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Similar:
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DeCS
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