1 / 1
|
DeCS
|
|
|
Descriptor English:
|
|
Ornithine Carbamoyltransferase
|
Descriptor Spanish:
|
|
Ornitina Carbamoiltransferasa
|
Descriptor Portuguese:
|
|
Ornitina Carbamoiltransferase
|
Synonyms English:
|
|
Carbamoyltransferase, Ornithine
Carbamylphosphate Transferase, Ornithine
Ornithine Carbamylphosphate Transferase
Ornithine Transcarbamylase
Transcarbamylase, Ornithine
Transferase, Ornithine Carbamylphosphate
|
Tree Number:
|
|
D08.811.913.555.275.600
|
Definition English:
|
|
A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3. |
Entry Combination - descr/qualif English:
|
|
Ornithine Carbamoyltransferase/deficiency use Ornithine Carbamoyltransferase Deficiency Disease
|
See Related English:
|
|
Ornithine Carbamoyltransferase Deficiency Disease
|
History Note English:
|
|
1965(1964)
|
Allowable Qualifiers English:
|
|
|
Record Number:
|
|
10132
|
Unique Identifier:
|
|
D009954
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|