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DeCS
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Descriptor English:
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Copper-transporting ATPases
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Descriptor Spanish:
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ATPasas Transportadoras de Cobre
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Descriptor Portuguese:
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ATPases Transportadoras de Cobre
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Synonyms English:
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ATP7A Protein
ATP7B Cu binding P type ATPase
ATP7B Cu-binding P type ATPase
ATPase 1, Copper-transporting
ATPase Copper Transporting alpha
ATPase, Copper-transporting
ATPase, Cu++ transporting, beta Polypeptide (Wilson Disease)
ATPase, Pineal Night-specific
ATPases, Copper-transporting
ATPases, Cu-transporting
Adenosine Triphosphatases, Copper-transporting
Copper Pump 1
Copper transporting ATPase
Copper transporting ATPase 1
Copper transporting ATPase 2
Copper transporting ATPases
Copper transporting Adenosine Triphosphatases
Copper-transporting ATPase
Copper-transporting ATPase 1
Copper-transporting ATPase 2
Copper-transporting Adenosine Triphosphatases
Cu transporting ATPases
Cu(+)-transporting ATPases
Cu-transporting ATPases
Menkes Disease associated Protein
Menkes Disease-associated Protein
Night-specific ATPase, Pineal
PINA Enzyme
Pineal Night specific ATPase
Pineal Night-specific ATPase
Triphosphatases, Copper-transporting Adenosine
Wilson Disease Cu binding P Type ATPase
Wilson Disease Cu-binding P Type ATPase
Wilson Disease Protein
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Tree Number:
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D08.811.277.040.025.314.500
D12.776.157.530.450.250.656
D12.776.157.530.813.500
D12.776.543.585.450.250.656
D12.776.543.585.813.500
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Definition English:
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P-type ATPases which transport copper ions across membranes in prokaryotic and eukaryotic cells. They possess a conserved CYSTEINE-HISTIDINE-SERINE (CPx) amino acid motif within their transmembrane helices that functions in cation translocation and catalytic activation, and an N-terminal copper-binding CxxC motif that regulates enzyme activity. They play essential roles in intracellular copper homeostasis through regulating the uptake, efflux and storage of copper ions, and in cuproprotein biosynthesis. |
See Related English:
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Hepatolenticular Degeneration
Menkes Kinky Hair Syndrome
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History Note English:
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2018 (1994)
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Allowable Qualifiers English:
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Record Number:
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56998
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Unique Identifier:
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D000073840
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Occurrence in VHL:
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Similar:
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DeCS
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